Pseudomyogenic
hemangioendothelioma affects people at many ages, with a mean age in the third or early forth decades, (1,3,5) and has a striking male predominance.
infantile
hemangioendothelioma of the liver: a radiologic-pathologic-clinical correlation.
Keratins MNF116 and CAM5.2, epithelial membrane antigen (EMA), CD31, and CD34 were also negative, as was CAMTA1, a recently described antibody expressed in epithelioid
hemangioendothelioma (Table 1 and Fig.
Epithelioid
hemangioendothelioma: a vascular tumor often mistaken for a carcinoma.
The suffix "oma" is typically associated with tumors, and is appropriately reserved for the vascular tumors such as hemangioma and
hemangioendothelioma. A summary of the modifications in terminology for some of the most common lesions is presented in Table 4.
Categorization of benign and malignant aspirates in two time periods Hepatic 2011-2013 2015-2016 lesion (without ROSE) (with ROSE) Inadequate 22 6 Benign 1 Normal liver/reactive 19 32 hepatocytes 2 Regenerative nodule 9 2 3 Pyogenic abscess 6 4 4 Amoebic liver abscess 2 0 5 Aspergillus 0 1 Malignant 1 90 65 2 Metastatic deposits 4 7 Malignant, not otherwise 3 specified 8 24 4 Hepatocellular carcinoma 0 1 Total
Hemangioendothelioma 160 142 (*) Rapid on-site evaluation (ROSE)
Masson intravascular
hemangioendothelioma. Urology.
In 1986, Weiss and Enzinger [13] described a unique vascular tumor as
hemangioendothelioma with combined features of cavernous hemangioma and Kaposi's sarcoma.
described a series of six patients with a leiomyosarcoma and one with
hemangioendothelioma. In their series, the median survival was reported as 31 months [5].
The clinical differential diagnosis of subcutaneous LCH includes a wide variety of subcutaneous pathologies, including but not limited to vascular malformation, Kaposiform
hemangioendothelioma, and infantile hemangioma.
Vascular malformations include slow-flow malformations (with venous, capillary and/or lymphatic components) and fast-flow malformations (with arterial components); while vascular neoplasms undergo mitosis and include such lesions as infantile hemangioma, congenital hemangioma, kaposiform
hemangioendothelioma, tufted angioma, hemangiopericytoma, and angiosarcoma [2].
Epithelioid
hemangioendothelioma (EHE) is a rare vascular neoplasm that occurs more often in women than men and usually arises within the liver, but can also present within other tissues including lung, bone, or peritoneum [1].