hemangioblastoma

[he-man″je-o-blas-to´mah]

a benign blood vessel tumor of the cerebellum, spinal cord, or retina, consisting of proliferated blood vessel cells and angioblasts. Those arising in the cerebellum (cerebellar hemangioblastoma) may be cystic and associated with von hippel-lindau disease. Called also angioblastoma.

cerebellar hemangioblastoma hemangioblastoma of the cerebellum, often cystic; an autosomal dominant form is associated with von Hippel-Lindau disease.

he·man·gi·o·blas·to·ma

(he-man'jē-ō-blas-tō'mă),

A benign neoplasm frequently arising in the cerebellum composed of capillary vessel-forming endothelial cells and stromal cells; a slowly growing tumor that affects, primarily, middle-aged individuals; increased incidence in von Hippel-Lindau disease.

Synonym(s): angioblastoma, Lindau tumor

Farlex Partner Medical Dictionary © Farlex 2012

Hemangioblastoma

(1) A tumour of soft tissues, which is of intermediate aggressiveness and thus preferably known as hemangioendothelioma.
(2) A vascularised cerebellar tumour, representing 2% of CNS neoplasms, which occurs in the 3rd–4th decades, either alone or associated with von-Hippel-Lindau syndrome, phaeochromocytoma, syringomyelia or erythrocythemia.

Management
Excision.

Prognosis
Good.

he·man·gi·o·blas·to·ma

(hē-man'jē-ō-blas-tō'mă)

A benign cerebellar neoplasm composed of capillary vessel-forming endothelial cells and stromal cells; a slowly growing tumor that affects, primarily, middle-aged individuals; increased incidence in von Hippel-Lindau disease.
Synonym(s): angioblastoma, Lindau tumor, haemangioblastoma.

Medical Dictionary for the Health Professions and Nursing © Farlex 2012

Lindau,

Arvid Wilhelm, Swedish pathologist, 1892-1958.

Lindau disease - Synonym(s): von Hippel-Lindau syndrome

Lindau tumor - a benign cerebellar neoplasm. Synonym(s): hemangioblastoma

von Hippel-Lindau syndrome - see under von Hippel

Medical Eponyms © Farlex 2012

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References in periodicals archive

Cervical dumbbell intra-extradural hemangioblastoma: total removal through the lateral approach: technical case report.

SPINAL DUMBBELL EPIDURAL HEMANGIOMA: TWO STAGE/SAME SITTING/SAME POSITION POSTERIOR MICROSURGICAL AND TRANSTHORACIC ENDOSCOPIC RESECTION --CASE REPORT AND REVIEW OF THE LITERATURE

The cranial mass was excised and hemangioblastoma was diagnosed histologically.

Two Childhood Pheochromocytoma Cases due to von Hippel-Lindau Disease, One Associated with Pancreatic Neuroendocrine Tumor: A Very Rare Manifestation

VHL Type 1 is characterized by tumor structures such as central nervous system or retinal hemangioblastoma, but no pheochromocytoma.

Early-Onset Isolated Bilateral Pheochromocytoma As a Major Clinical Manifestation of von-Hippel Lindau Syndrome Type 2C

Metastatic clear cell renal cell carcinoma (CCRCC) can bear a striking similarity to hemangioblastoma. CCRCC is usually positive for PAX8 and CAIX and negative for S100 and inhibin-A.

Sporadic Retroperitoneal Hemangioblastoma: Report of a Case and Review of the Literature

Hemangioblastoma of spinal nerve: A report of six cases.

Sudden-onset paraplegia during pregnancy caused by haemorrhage in a spinal cord haemangioblastoma: A case report

For the central nervous system (CNS), it has been reported that screening hemangioblastomas in asymptomatic individuals was not indicated since surgery was considered only in symptomatic subjects.

Structured assessment and followup for patients with hereditary kidney tumour syndromes

The main diagnostic considerations are hemangioblastoma (particularly in the absence of homogenous enhancement), metastatic disease, ependymoma, or a choroid plexus tumor.

Intracranial Capillary Hemangioma in the Posterior Fossa of an Adult Male

Pathological satiety caused by brainstem hemangioblastoma. J Neurosurg Pediatr 2008;2: 397-401.

EXPERIENCE WITH ENDOSCOPIC THIRD VENTRICULOSTOMY IN THE MANAGEMENT OF HYDROCEPHALUS SECONDARY TO POSTERIOR FOSSA TUMOR

(2,4,10) The appearance of a cavernous malformation with edema may be unclear and mimic other lesions such as neoplasm, including ependymoma, astrocytoma, hemangioblastoma, metastasis, multiple sclerosis plaque, and arteriovenous malformation.

Spinal cord intramedullary cavernoma: a case report

(1.) Agostinelli C, Roncaroli F, Galassi E, Bernardi B, Acciarri N, Tani G: Leptomeningeal Hemangioblastoma: Case Illustration.

Supratentorial dural-based haemangioblastoma in a Native American patient without Von Hippel Lindau Syndrome