Cogan syndrome was initially suspected in view of the characteristic interstitial keratitis, fluctuating sensorineural hearing loss, and episodic vertigo.
When a review of the patient's ophthalmologic examination revealed that he suffered from recurrent iritis and not interstitial keratitis or uveitis, the diagnosis of Cogan syndrome was questioned.
In a literature review of 111 cases by Grasland et al., 54% and 37% of cases with typical and atypical Cogan syndrome remained deaf in both ears despite treatment [35].
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Nishi et al., "Childhood Cogan syndrome with aortitis and anti-neutrophil cytoplasmic antibody-associated glomerulonephritis," Pediatric Rheumatology, vol.
Kodati, "Lamotrigine-induced tubulointerstitial nephritis and uveitis-atypical Cogan syndrome," European Journal of Ophthalmology, vol.