Schilder disease

Schil·der dis·ease

(shil'der),

term used to describe at least two separate disorders described by Schilder: 1) Diffuse sclerosis or encephalitis periaxialis diffusa; a nonfamilial disorder affecting primarily children and young adults and characterized by progressive dementia, visual disturbances, deafness, pseudobulbar palsy, and hemiplegia or quadriplegia. Most patients die within a few years of onset; pathologically, there is a large, asymmetric area of myelin destruction, sometimes involving an entire cerebral hemisphere, and typically with extension across the corpus callosum. 2) The leukodystrophies.

Synonym(s): encephalitis periaxialis diffusa

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Schil·der dis·ease

(shil'dĕr di-zēz')

Term used to describe at least two separate disorders described by Schilder: 1) diffuse sclerosis or encephalitis periaxialis diffusa; a nonfamilial disorder affecting primarily children and young adults and characterized by progressive dementia, visual disturbances, deafness, pseudobulbar palsy, and hemiplegia or quadriplegia. Most patients die within a few years of onset; pathologically, there is a large, asymmetric area of myelin destruction, sometimes involving an entire cerebral hemisphere, and typically with extension across the corpus callosum. 2) the leukodystrophies.
Synonym(s): encephalitis periaxialis diffusa.

Medical Dictionary for the Health Professions and Nursing © Farlex 2012

Schilder,

Paul Ferdinand, Austrian neurologist, 1886-1940.

Addison-Schilder disease - Synonym(s): Schilder disease

Flatau-Schilder disease - Synonym(s): Schilder disease

Schilder disease - encephalitis periaxialis diffusa; progressive demyelinating disorder in adults; early symptom is visual impairment with mental deterioration. Synonym(s): Addison-Schilder disease; Flatau-Schilder disease; Schilder syndrome

Schilder encephalitis

Schilder syndrome - Synonym(s): Schilder disease

Medical Eponyms © Farlex 2012