von Recklinghausen's disease


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Related to von Recklinghausen's disease: Neurofibromatosis Type 1, Von Recklinghausen's disease of bone, NF-1

von Recklinghausen's disease

 [von rek´ling-how″zenz]

von Recklinghausen's disease

Neurofibromatosis, type 2 Neurology An AD condition characterized by cafe-au-lait skin spotting and pendulous fibrous tumors. See Neurofibromatosis.

von Recklinghausen's disease

See NEUROFIBROMATOSIS.
References in periodicals archive ?
It may be related to systemic disorders like MEN or neurofibromatosis syndrome (von Recklinghausen's disease), thus the importance of its accurate diagnosis.
Somatostatinoma of the papilla of Vater with multiple gastrointestinal stromal tumors in a patient with von Recklinghausen's disease. J Gastroenterol.
(4) According to Supance, Quenelle and Crissman, solitary neurofibroma of larynx are frequently present than combinedly occurring with von Recklinghausen's disease. (5) As the tumor is benign in nature, total excision conservatively is adequate.
Malignant schwannoma of the parapharyngeal space in von Recklinghausen's disease: A case report and review of the literature.
INTRODUCTION: Neurofibroma of small intestine are usually accompanied by Von Recklinghausen's disease (NF1) and usually originate in the intramuscular plexus of Auerbach.
Malignant peripheral nerve sheath tumors can arise de novo or as a result of the malignant transformation of a neurofibroma (von Recklinghausen's disease).
By definition they are confined and are seen in patients who do not suffer from Von Recklinghausen's Disease. According to Geschikter.
Malignant schwannoma of the sympathetic chain, combined with plexiform neurofibromas of the tongue and larynx in a patient with von Recklinghausen's disease. Eur Arch Otorhinolaryngol 1997;254:20-1.
There was no family history of Von Recklinghausen's disease.