urticaria pigmentosa


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Related to urticaria pigmentosa: Systemic mastocytosis

urticaria

 [ur″tĭ-ka´re-ah]
a vascular reaction of the skin marked by transient appearance of slightly elevated patches (wheals) that are redder or paler than the surrounding skin and often attended by severe itching; the cause may be certain foods, infection, or emotional stress. (See Atlas 2, Plate D.) Called also hives. adj., adj urtica´rial.
cold urticaria urticaria precipitated by cold air, water, or objects, occurring in two forms: In the autosomal dominant form, which is associated with fever, arthralgias, and leukocytosis, the lesions occur as erythematous, burning papules and macules. The more common acquired form is usually idiopathic and self-limited.
giant urticaria angioedema.
urticaria hemorrha´gica purpura with urticaria.
urticaria medicamento´sa that due to use of a drug.
papular urticaria (urticaria papulo´sa) an allergic reaction to the bite of various insects, with appearance of lesions that evolve into inflammatory, increasingly hard, red or brownish, persistent papules.
urticaria pigmento´sa the most common form of mastocytosis, occurring primarily in children, manifested as persistent pink to brown macules or soft plaques of various size; pruritus and urtication occur on stroking the lesions.
urticaria pigmentosa, juvenile urticaria pigmentosa present at birth or in the first few weeks of life, usually disappearing before puberty, taking the form of a single nodule or tumor or of a disseminated eruption of yellowish brown to yellowish red macules, plaques, or bullae.
solar urticaria a rare form produced by exposure to sunlight.

ur·ti·car·i·a pig·men·to·'sa

cutaneous mastocytosis resulting from an excess of mast cells in the superficial dermis, producing a chronic eruption characterized by flat or slightly elevated brownish papules that urticate when stroked. The disease in children frequently involutes spontaneously whereas resolution is rare with adult onset and there may be systemic lesions.
See also: diffuse cutaneous mastocytosis.

urticaria pigmentosa

An idiopathic self-limiting condition characterised by light brown welts, intense itching and hives. By age 2, affected children develop mast cell-rich lesions which produce histamine and cause the typical skin response; rubbed lesions rapidly develop a wheal and systemic symptoms (flushing, headache, diarrhoea, tachycardia, and fainting); younger children may develop fluid-filled blisters over a traumatised lesion. It often disappears by puberty.

urticaria pigmentosa

Dermatology An idiopathic self-limiting benign condition characterized by light brown skin lesions, intense itching, and hives at the site of rubbed lesions; affected children develop by age 2 lesions containing mast cells which produce histamine and cause the typical skin response–rubbed lesions rapidly develop a wheal and systemic Sx–flushing, headache, diarrhea, tachycardia, fainting; younger children may develop a fluid-filled blister over a traumatized lesion; UP often disappears by puberty. See Histamine, Mastocytosis.

ur·ti·ca·ria pig·men·to·sa

(ŭr'ti-kar'ē-ă pig'men-tō'să)
Cutaneous mastocytosis resulting from an excess of mast cells in the superficial dermis, producing a chronic eruption characterized by flat or slightly elevated brownish papules that urticate when stroked.

Nettleship,

Edward, English ophthalmologist and dermatologist, 1845-1913.
Nettleship dilator
Nettleship iris repositor
Nettleship syndrome - pigmented nodules or macules. Synonym(s): urticaria pigmentosa
References in periodicals archive ?
In conclusion, according to the clinical presentation, positive Darier's sign, elevated serum tryptase levels, and the presence of mast cells in the papillary dermis histopathologically, the diagnosis of urticaria pigmentosa was confirmed.
Neonatal bullous urticaria pigmentosa: case report.
Anesthetic management of a labouring parturient with urticaria pigmentosa. Can J Anaesth 2006; 53:380-384.
Case 4: A 40-year-old physician had urticaria pigmentosa and severe back pain and vertebral fractures sustained after heavy lifts (Table I).
Case 5: A 47-year old general labourer and ski runner with a 20-year history of urticaria pigmentosa had noticed aching pain in the back after exertion resulting in vertebral fractures (Table I).
Two patients diagnosed with urticaria pigmentosa had a positive familial history (father in one patient and sibling in one patient).
The most commonly reported type of cutaneous mastocytosis is urticaria pigmentosa. In the study of Hannaford et al.
Based on the history and clinical examination the diagnosis of urticaria pigmentosa was made and for confirmation, skin biopsy was performed from one of the lesions on the trunk.
The commonest form of cutaneous mastocytosis is urticaria pigmentosa.3 It develops in the first year of life in 84% of children in one study.4 The adult onset is between 20-40 years.5 The disease manifests as numerous reddish-brown, monomorphic maculopapules or plaques, distributed symmetrically over the entire body except the face, head, palms and soles.6 To our knowledge this is the first case report of urticaria pigmentosa with involvement of palms and soles.