KMS is not associated with infantile hemangiomas (which are common benign vascular lesions) but occurs almost exclusively as a complication of other rare entities such as kaposiform hemangioendotheliomas (KHE) and tufted angiomas (TA).
The diagnosis of littoral cell angioma (LCA) was finally made, which is a different vascular tumor with a resemblance pathologically to either tufted angioma (TA) or kaposiform hemangioendothelioma (KHE) in association with lymphatic-like vessels .
Kasabach-Merritt Syndrom arising from a tufted angioma successfully treated with systemic corticosteroid.
Variable response to propranolol treatment of kaposiform hemangioendothelioma, tufted angioma and Kasabach-Merritt syndrome.
These are known as giant tufted angiomas. Our case was an 11-year- old boy presenting with a large indurated plaque over right lumbar region which was diagnosed as tufted angioma on histopathology.
Tufted angioma is an uncommon benign vascular tumour encountered usually in infancy and early childhood.
Tufted angioma (TA) is a rare benign cutaneous vascular neoplasm.
A diagnosis of tufted angioma was made and the patient was referred to the Surgery department for necessary management.
Tufted angioma has been described in the literature under different names including Nakagawa's angioma, Nakagawa's angioblastoma, progressive capillary hemangioma, and acquired tufted angioma of the skin and subcutaneous tissue.2 It is a rare, benign vascular tumour occurring most commonly in prepubertal children.3 A few cases occurring at unusual sites like oral mucosa in adults have been reported.4 The lesion of TA enlarges slowly over 5 months to 10 years after which no further growth occurs.
Tufted angioma is a rare entity and the giant variety is even rarer.
Alessi E, Bertani E, Sola F: Acquired tufted angioma. Am J Dermatopathol.