true hermaphroditism


Also found in: Dictionary, Thesaurus, Encyclopedia, Wikipedia.

hermaphroditism

 [her-maf´ro-di-tizm″]
presence of both ovarian and testicular tissue and of ambiguous morphologic criteria of sex, a rare condition in human beings. Hermaphroditism is not to be confused with pseudohermaphroditism, in which an individual has only one kind of gonad but has significant secondary sex characters typical of the opposite sex.
bilateral hermaphroditism that in which gonadal tissue typical of both sexes occurs on each side of the body.
false hermaphroditism pseudohermaphroditism.
lateral hermaphroditism presence of gonadal tissue typical of one sex on one side of the body and typical of the other sex on the opposite side.
transverse hermaphroditism that in which the external genital organs are typical of one sex and the gonads typical of the other sex.
true hermaphroditism coexistence in the same person of both ovarian and testicular tissue, with somatic characters typical of both sexes.
unilateral hermaphroditism presence of gonadal tissue typical of both sexes on one side and of only an ovary or a testis on the other.

true her·maph·ro·dit·ism

[MIM*235600]
hermaphroditism in which both ovarian and testicular tissue are present. Somatic characteristics of both sexes are present; also called true intersexuality.

true hermaphroditism

Endocrinology A condition in which one person has ovarian and testicular tissue, genotypically either 46, XX or 46, XY; 50% to 75% are raised as boys; testicular tissue is dysgenic, doesn't produce sperm and may undergo malignant degeneration–requiring prophylactic removal; ovarian function in those raised as girls may be adequate to produce term pregnancy. See Hermaphroditism, Intersex disorder.

true her·maph·ro·di·tism

(trū hĕr-mafrō-dīt-izm)
Condition in which both ovarian and testicular tissue are present. Somatic characteristics of both sexes are present; also called true intersexuality.
References in periodicals archive ?
True hermaphroditism results in the presence of both testis and ovarian tissue also called ovotestis, and occur in less than 10% of disorders of sexual differentiation cases.1 About 90% of cases, patients have 46 XX karyotype.
XX true hermaphroditism in southern African blacks: exclusion of SRY sequences and uniparental disomy of the X chromosome.
True hermaphroditism and mixed gonadal dysgenesis in young children.
Diseases causing clitoral hypertrophy include congenital adrenal hyperplasia, true hermaphroditism, mixed gonadal dysgenesis, and congenital idiopathic clitoral hypertrophy, and the 3 former diseases account for 95% of cases.
Garewal, "True hermaphroditism: clinical profile and management of six patients from North India," Journal of Obstetrics and Gynaecology, vol.
The disorders of sex development are now broadly grouped into three main diagnostic categories namely 46 XY DSD (previously called male Pseudo hermaphroditism), 46 XX DSD (previously called female Pseudo hermaphroditism) and sex chromosome DSD (previously called true hermaphroditism).
True hermaphroditism in an XY individual due to a familial point mutation of the SRY gene.