tricuspid atresia


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Related to tricuspid atresia: Fontan procedure

atresia

 [ah-tre´zhah]
congenital absence or closure of a normal body opening or tubular structure; see also obstruction. adj., adj atret´ic.
anal atresia (atresia a´ni) imperforate anus.
aortic atresia
1. congenital absence of the aortic orifice.
2. absence or closure of the aortic orifice, a rare congenital anomaly in which the left ventricle is hypoplastic, so that oxygenated blood passes from the left into the right atrium through a septal defect, and the mixed venous and arterial blood passes from the pulmonary artery to the aorta by way of a patent ductus arteriosus.
aural atresia absence of closure of the auditory canal.
biliary atresia congenital obliteration or hypoplasia of one or more components of the bile ducts, resulting in persistent jaundice and liver damage.
choanal atresia blockage of the posterior nares. When the blockage is bilateral in a newborn, it produces acute respiratory distress because neonates are nose-breathers. Diagnosis is confirmed if a catheter cannot be passed through the nares. Until surgery is done to relieve the obstruction, insertion of an airway may be necessary.
esophageal atresia congenital lack of continuity of the esophagus, commonly accompanied by tracheoesophageal fistula, and characterized by accumulations of mucus in the nasopharynx, gagging, vomiting when fed, cyanosis, and dyspnea. Treatment should begin with suction of the upper esophageal pouch, followed by surgical repair by esophageal anastomosis and division of the fistula as soon as the infant's general condition permits.
follicular atresia (atresia folli´culi) the normal death of the ovarian follicle when unfertilized.
laryngeal atresia congenital lack of the normal opening into the larynx.
mitral atresia congenital obliteration of the mitral orifice; it is associated with hypoplastic left heart syndrome and transposition of great vessels.
prepyloric atresia congenital membranous obstruction of the gastric outlet, characterized by vomiting of gastric contents only. Called also pyloric atresia.
pulmonary atresia congenital severe narrowing or obstruction of the pulmonary orifice, with cardiomegaly, reduced pulmonary vascularity, and right ventricular atrophy. It is usually associated with tetralogy of fallot, transposition of great vessels, or other cardiovascular anomalies.
pyloric atresia prepyloric atresia.
tricuspid atresia absence of the tricuspid orifice, circulation being made possible by an atrial septal defect.
 Tricuspid atresia, here displaying a ventricular septal defect and normally related great arteries, the arrows showing the altered flow of blood through the heart. From Dorland's, 2000.
urethral atresia imperforation of the urethra.

tri·cus·pid a·tre·si·a

[MIM*605067]
congenital lack of the tricuspid orifice.

tricuspid atresia

Cardiology A rare congenital heart disease characterized by obstruction of blood flow from the right atrium to the right ventricle, by an absent or abnormally developed tricuspid valve, which compromises pulmonary blood flow; to maintain pulmonary blood flow, blood from the right atrium flows through the foramen ovale into the left atrium, then the left ventricle, then part of the blood flows directly into the right ventricle through a patent VSD or out the aorta via PDA allowing part of the aortic blood flow to flow into the pulmonary artery; this supplies the lungs with some, less than optimal, blood flow; it also puts a strain on the left ventricle which must pump both systemic and pulmonary blood Clinical Cyanosis, limited exercise tolerance, SOB. See Patent ductus arteriosus, Ventricular septal defect.

tri·cus·pid a·tre·si·a

(trī-kŭs'pid ă-trē'zē-ă)
Congenital lack of the tricuspid orifice.
References in periodicals archive ?
Our case had a rare association of tricuspid atresia and atrial septal aneurysm (type 2L) along with pulmonary stenosis.
Harry has a heart defect called tricuspid atresia, which means his right valve, one of two vital to pumping blood around his body, does not work, and he has a hole in his heart.
This suggests the large right atrium of tricuspid atresia or pulmonary atresia with intact ventricular septum.
She had tricuspid atresia, the 14th-most-common congenital heart disease.
Among the 9 survivors are 4 patients with Ventricular septal defect, 1 patient with OS- ASD, 2 with Tricuspid atresia, 1 with Tetralogy of fallot and 1 patient with Tachyarrhythmia.
Deborah was born with tricuspid atresia, a rare condition in which one side of the heart fails to develop properly.
Also ASD+VSD, ASD+VSD + PS, PDA+PS, tricuspid atresia (TA), PS, atrioventricular septal defect (AVSD), coarctation of the aorta (CoA), tetralogy of Fallot (TOF), and transposition of the great arteries (TGA) were observed each in one patient.
A 10-year-old patient with tricuspid atresia, ventricular septal defect and severe pulmonary stenosis had underwent a left modified Blalock-Taussig shunt on the 7th day of life.
The concomitant congenital valvular abnormalities described to date consist of mitral atresia, double-orifice mitral valve, mitral valve cleft, congenital mitral valve stenosis, aortic stenosis, absent aortic valve and tricuspid atresia, which all have been primarily reported in infants and children (2,5,8).