The benign tumors are: Trichofolliculoma, Pilar sheath acanthoma, Fibrofolliculoma, Trichodiscoma
, Trichoepithelioma, Trichoblastoma, Trichoadenoma, Pilomartricoma, Trichilemmoma, Trichilemmal horn and Proliferating trichilemmal cyst.
40) Patients may also develop associated skin manifestations, including cutaneous fibrofolliculomas, trichodiscomas
, and perifollicular fibromas, and are potentially at risk of melanoma.
Acrochordons are one of the components of Birt-Hogg-Dune syndrome, the other components being fibrofolliculomas and trichodiscomas
This condition is associated with kidney cancer and is marked by benign fibrofolliculomas and trichodiscomas
that most often occur on the head and neck.
Birt-Hogg-Dube (BHD) syndrome is a rare condition inherited in an autosomal-dominant fashion and characterized by unique skin lesions (multiple fibrofolliculomas, trichodiscomas
, and acrochordons) and associated internal organ lesions, such as intestinal polyps, renal and lung cysts, and medullary thyroid carcinoma in the original description.