Mounier-Kuhn syndrome or congenital tracheobronchomegaly: A literature review.
Mounier-Kuhn syndrome: report of 8 cases of tracheobronchomegaly with associated complications.
Lau, "Primary tracheobronchial amyloidosis associated with tracheobronchomegaly
evaluated by novel four-dimensional functional CT," Respirology Case Reports, vol.
Buls, "Mounier-Kuhn syndrome or congenital tracheobronchomegaly: a literature review," Respiratory Medicine, vol.
Garces-Inigo et al., "Tracheobronchomegaly following intrauterine tracheal occlusion for congenital diaphragmatic hernia," Pediatric Radiology, vol.
Mounier-Kuhn syndrome (MKS) also known as tracheobronchomegaly is an uncommon condition characterized by dilatation of the trachea and major bronchi.
Bronchial and tracheal diverticula can also accompany tracheobronchomegaly. Sarcoidosis, usual interstitial pneumonia, and cystic fibrosis can cause severe fibrosis of the upper lobes, which may result in tracheal enlargement if there is sufficient tracheal traction.
Tracheobronchomegaly. Chest 1994; 106 (5): 1589-90.
Mounier-Kuhn syndrome: a case report (tracheobronchomegaly) [in Turkish].
(Mounier-Kuhn syndrome) is characterized by diffuse airway dilatation, which makes it unique from the other morphologic abnormalities of the central airways.
Tracheal diverticula and tracheobronchomegaly
. Dis Chest 1966;49:345-51.
The clinical differential diagnosis includes tracheobronchomegaly
and tracheomalacia, both of which manifest as a softening, flexibility, or dilation of the trachea, as opposed to the rigidity of tracheopathia osteoplastica.