It also revealed taurodontism
with molar teeth in the maxillary arch and underdeveloped mandibular ridge (Figure No.
is characterized by an enlarged pulp chamber with apical displacement of pulp floor and absence of cementoenamel junction constriction diagnosed by radiographic examination.
Abnormal tooth eruption, morbid root and coronal resorption, congenitally missing teeth, malocclusion, anterior open bites, pulpal calcification, dentin dysplasia, hypercementosis, root malformation, and taurodontism
have been commonly seen.
Additional unusual dental findings such as single-rooted funnel-shaped molars, reduced crown size, enamel hypoplasia, supernumerary teeth, dental fusion, taurodontism
, abnormal occlusal anatomy with wide grooves, and atypical cusps have been reported in most previous cases of this syndrome.
The frequency of other anomalies was as follows: molar-incisor hypomineralization 0.25%, turner hypoplasia 0.1%, fluorosis 0.1%, odontoma 0.1%, fusion 0.09%, gemination 0.06%, amelogenesis imperfecta 0.05%, dens invaginatus 0.03%, talon cusp 0.02%, taurodontism
0.02%, macrodontia 0.02%, dentinogenesis imperfecta 0.02%, dilaceration 0.02%, ectopic eruption 0.01% and microdontia 0.01%.
In addition, an association between taurodontism
and hypodontia was found in a Dutch study, where taurodontism
of the lower first molars was present in 29% of oligodontia patients but only 10% of controls .
A correlation has been determined between the presence of denticles and the enamel pearls, taurodontism
, dilaceratio and crooked roots .
Other abnormalities like alopecia, taurodontism
, mental retardation, small genitals, premature aging, nutmeg liver, horseshoe kidneys, amyloidosis, and development of Hodgkin's disease and adenocarcinoma have also been reported, (12,16) but not observed in this patient.
Such abnormalities may include peg-shaped incisors, long thin-rooted teeth, malformed molars, microdontia, enamel hypoplasia, shallow cusps, taurodontism
and partial anodontia [Levy, 1967].
More recently, taurodontism
of the first lower molar was detected in 24.8% of patients with congenital tooth loss, and first molar infraochlesis was detected in 65.7% of the same samples (Rubenstein et al., 1991; Bruce et al., 1994).