superficial angiomyxoma

superficial angiomyxoma

A solitary, slow-growing, infiltrative superficial tumour averaging 3.5 cm, which is found on the trunk, genitalia, head and neck, and limbs, and is classically associated with Carney complex.

Management
Surgery; no recurrence.
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References in periodicals archive ?
There are 5 entities commonly accepted as myxomas: intramuscular myxoma, juxta articular myxoma, superficial angiomyxoma (or cutaneous myxoma), aggressive angiomyxoma (usually pelvic and perineal regions) and myxoma of nerve sheath (myxoid neurothekeoma).
The differential diagnosis of AAM includes angiomyofibroblastoma, superficial angiomyxoma, fibroepithelial stromal polyps, myxoid lipomatous tumors, and myxoid leiomyoma.
4) Superficial angiomyxoma has a nonspecific immunophenotype but is generally negative for estrogen receptor and progesterone receptor and may be immunoreactive for S100.
The differential diagnoses of SAFM include CD34-immunopositive neoplasms, such as dermatofibrosarcoma protuberans, superficial angiomyxoma, and myxoid neurofibroma, and CD34-immunonegative neoplasms, such as giant cell tumor of the tendon sheath, glomus tumor, sclerosing perineuroma, fibrous histiocytoma, and acral fibrokeratoma.
Because of their CD34 positivity and the presence of spindle-shaped and stellate cells embedded in a vascular, basophilic matrix, SAFMs can be confused with superficial angiomyxomas.
8] Although this lesion has much microscopic overlap with our case, superficial angiomyxoma has a characteristic nodular architecture, acellular myxoid clefts, and is grossly well-demarcated; none of these features was seen in our case.