sugar tumor

sug·ar tu·mor

a benign clear cell tumor of the lung containing abundant glycogen.
A benign, circumcised but unencapsulated lung tumour characterised by exuberant vascularity, little stroma and round, polygonal glycogen-filled clear cells with well-defined borders. Sugar tumours may be surrounded by hyalinised boundaries with focal calcifications and ‘spider’ cells. They are classified as PEComas. The tumours are HMB45 +, PAS +ve and dPAS -ve
References in periodicals archive ?
1) The PEComa family includes angiomyolipoma, clear cell sugar tumor of the lung, lymphangioleiomyomatosis, clear cell myomelanocytic tumor of the falciform ligament/ligamentum teres, and rare clear cell tumors of other anatomic sites.
Comparison of melanoma antigen recognized by T cells (MART-1) to HMB-45: additional evidence to support a common lineage for angiomyolipoma, lymphangiomyomatosis, and clear cell sugar tumor.
Primary extrapulmonary sugar tumor (PEST): a report of four cases.
The PEComa family of tumors includes angiomyolipoma, lymphangioleiomyomatosis, clear cell sugar tumor of the lung, and clear cell myomelanocytic tumor of the falciform ligament/ligamentum teres.
1) In 1991, Pea and colleagues (2) first noted this unusual cell in both angiomyolipoma (AML) and clear cell sugar tumor (CCST) of the lung.
Comparison of melanoma antigen recognized by T-cells (MART-1) to HMB-45: additional evidence to support a common lineage for angiomyolipoma, lymphangiomyomatosis, and clear cell sugar tumor.
It also should be noted that A103 immunostaining may be seen in angiomyolipomas, lymphangioleiomyomatosis, clear cell sugar tumors, and extra-adrenal steroid-producing tumors such as Leydig cell tumors and granulosa cell tumors.