Steatocystoma multiplex may be associated with eruptive vellus hair cysts and pachyonychia congenita (nail and teeth abnormalities and palmoplantar keratoderma).
If there is a single steatocystoma, it is called steatocystoma simplex.
Caption: Steatocystoma multiplex was diagnosed in this patient
Each steatocystoma is associated with a hair follicle, which can result in retention of trapped vellus hairs in the cystic lumen, as seen in our first patient [1,2,7].
Our report details two cases of uncommon pilosebaceous tumors, steatocystoma multiplex, and eruptive vellus hair cysts.
A classification can be made: localized, generalized; facial, acral, and the suppurative types; solitary lesions are known as Steatocystoma simplex .
Steatocystoma multiplex can be associated with pachyonychia congenita type 2 (which is characterized by hypertrophic nail dystrophy, focal keratoderma, multiple pilosebaceous cysts, and myriad conditions associated with ectodermal dysplasia) or eruptive vellus hair cysts [1,5].
multiplex is typically characterized by firm, yellow-to-flesh-colored dermal cysts ranging from a few millimeters to 1 cm in size.
In the case associated with steatocystoma multiplex, there was epithelioid cell reaction around the lesion but no foreign body type reaction directly against the myospherules.
Spherulocystic disease ("myospherulosis") arising in a lesion of steatocystoma multiplex.