spherophakia

spherophakia

 [sfe″ro-fa´ke-ah]
a developmental defect in which a smaller, more spherical optic lens than normal is formed, with partial or complete aplasia of the zonule.

sphe·ro·pha·ki·a

(sfē'rō-fā'kē-ă),
A congenital bilateral aberration in which the lenses are small, spheric, and subject to subluxation; may occur as an independent anomaly or may be associated with the Weill-Marchesani syndrome.
[sphero- + G. phakos, lens]

sphe·ro·pha·ki·a

(sfēr'ō-fā'kē-ă)
A congenital bilateral aberration in which the lenses are small, spheric, and subject to subluxation; may occur as an independent anomaly or may be associated with the Weill-Marchesani syndrome.
[sphero- + G. phakos, lens]

spherophakia 

A congenital, bilateral defect in which the crystalline lens is smaller and more spherical than normal. The zonule of Zinn may also be defective or absent. See Weill-Marchesani syndrome.
References in periodicals archive ?
The anterior chamber maintainer, which facilitates ophthalmological surgical procedures and reduces iatrogenic damage to the iris, corneal endothelium, and lens, has been used in the management of hard nuclear cataract lens [3], subluxation in young patients [4], endoscopic goniotomy [5], traumatic hyphaemas [6], congenital pupillary-irislens membrane [7], and spherophakia [8].
Khatib, "Vitrectorhexis and lens aspiration with posterior chamber intraocular lens implantation in spherophakia," Journal of Cataract and Refractive Surgery, vol.
Willoughby and Wishart (14) described a case of spherophakia with glaucoma whose IOP was successfully controlled following lensectomy without additional medication.
Spherophakia in a Newfoundland family: 8 years' experience.
Spherophakia with brachydactyly; comparison with Marfan's syndrome.
Lensectomy in the management of glaucoma in spherophakia. J Cataract Refract Surg.
(28) Myopia may result from degeneration of zonular fibres, resulting in a release of zonular tension, which allows spherical deformation of the lens (spherophakia).