spherophakia

spherophakia

 [sfe″ro-fa´ke-ah]
a developmental defect in which a smaller, more spherical optic lens than normal is formed, with partial or complete aplasia of the zonule.
Miller-Keane Encyclopedia and Dictionary of Medicine, Nursing, and Allied Health, Seventh Edition. © 2003 by Saunders, an imprint of Elsevier, Inc. All rights reserved.

sphe·ro·pha·ki·a

(sfē'rō-fā'kē-ă),
A congenital bilateral aberration in which the lenses are small, spheric, and subject to subluxation; may occur as an independent anomaly or may be associated with the Weill-Marchesani syndrome.
[sphero- + G. phakos, lens]
Farlex Partner Medical Dictionary © Farlex 2012

sphe·ro·pha·ki·a

(sfēr'ō-fā'kē-ă)
A congenital bilateral aberration in which the lenses are small, spheric, and subject to subluxation; may occur as an independent anomaly or may be associated with the Weill-Marchesani syndrome.
[sphero- + G. phakos, lens]
Medical Dictionary for the Health Professions and Nursing © Farlex 2012

spherophakia 

A congenital, bilateral defect in which the crystalline lens is smaller and more spherical than normal. The zonule of Zinn may also be defective or absent. See Weill-Marchesani syndrome.
Millodot: Dictionary of Optometry and Visual Science, 7th edition. © 2009 Butterworth-Heinemann
References in periodicals archive ?
The anterior chamber maintainer, which facilitates ophthalmological surgical procedures and reduces iatrogenic damage to the iris, corneal endothelium, and lens, has been used in the management of hard nuclear cataract lens [3], subluxation in young patients [4], endoscopic goniotomy [5], traumatic hyphaemas [6], congenital pupillary-irislens membrane [7], and spherophakia [8].
Khatib, "Vitrectorhexis and lens aspiration with posterior chamber intraocular lens implantation in spherophakia," Journal of Cataract and Refractive Surgery, vol.
Willoughby and Wishart (14) described a case of spherophakia with glaucoma whose IOP was successfully controlled following lensectomy without additional medication.
Spherophakia in a Newfoundland family: 8 years' experience.
Spherophakia with brachydactyly; comparison with Marfan's syndrome.
Lensectomy in the management of glaucoma in spherophakia. J Cataract Refract Surg.
(28) Myopia may result from degeneration of zonular fibres, resulting in a release of zonular tension, which allows spherical deformation of the lens (spherophakia).