scleromyxedema

scleromyxedema

 [skle″ro-mik″sĕ-de´mah]
a variant of lichen myxedematosus characterized by a generalized eruption of the nodules and diffuse thickening of the skin.
Miller-Keane Encyclopedia and Dictionary of Medicine, Nursing, and Allied Health, Seventh Edition. © 2003 by Saunders, an imprint of Elsevier, Inc. All rights reserved.

scle·ro·myx·e·de·ma

(sklē'rō-mik-se-dē'mă),
Generalized lichen myxedematosus with diffuse thickening of the skin underlying the papules.
Farlex Partner Medical Dictionary © Farlex 2012

Arndt,

Georg, German dermatologist, 1874-1929.
Arndt-Gottron syndrome - generalized lichen myxedematosus with diffuse thickening of the skin underlying the papules. Synonym(s): scleromyxedema
Medical Eponyms © Farlex 2012
References in periodicals archive ?
We took into consideration for differential diagnosis several scleroderma-like disorders: eosinophilic fasciitis, localized and systemic sclerosis, nephrogenic systemic fibrosis, scleromyxedema, scleredema and eosinophilia myalgia syndrome.
They often have antibodies to Scl-70.2 SSc mimics many other skin conditions like generalized morphea, scleromyxedema, scleredema of Buschke, primary systemic amyloidosis, chronic graft-versus-host disease, eosinophilic fasciitis etc.3 The criteria for diagnosis of systemic sclerosis have been established by the subcommittee for scleroderma criteria of American Rheumatism Association (now called the American College of Rheumatology).4
Scleromyxedema is also known as generalized lichen myxedematosus (LM).
It is also an endothelial marker and stains solitary fibrous tumor, spindle cell lipoma, superficial acral fibromyxoma, sclerotic fibroma, Kaposi sarcoma, neurofibroma, tricholemmoma, scleromyxedema, and nephrogenic systemic fibrosis, among others.
Pope: Systemic sclerosis can be confused with such sclerodermalike skin disorders as eosinophilic fasciitis (EF), morphea, scleromyxedema, and nephrogenic systemic fibrosis (NSF).
Histopathologically, the changes resembled scleromyxedema, a rare fibrosing disorder of the skin characterized by the deposition of collagen and mucin in association with a mixed inflammatory infiltrate containing numerous plasma cells.
Systemic sclerosis must be differentiated from other conditions associated with skin fibrosis, including localized scleroderma, scleredema, scleromyxedema, and eosinophilic fasciitis, as well as rare conditions (e.g., porphyria, cutaneous amyloidosis, progerias, and the stiff skin syndrome).
Due to its similarities to scleromyxedema and its occurrence only in patients undergoing dialysis, this new disorder was initially described as "scleromyxedema-like cutaneous disease of dialysis" (Cowper, 2003, p.
of cases Multiple myeloma 330 NSMM 20 Osteosclerotic myeloma 15 SMM 72 Indolent/evolving myeloma 8 Plasmacytoma (solitary) 22 Extramedullary myeloma 5 Multiple solitary plasmacytoma 3 Macroglobulinemia 9 IgM lymphoproliferative disease 2 IgM lymphoma 5 Smoldering macroglobulinemia 2 Primary systemic amyloidosis 269 LCDD 7 MGUS 114 Idiopathic Bence Jones proteinuria 4 Heavy chain disease 2 Cryoglobulinemia 4 Acquired Fanconi syndrome 3 Scleromyxedema 2 Plasma cell leukemia 1 Table 2.
Although nephrogenic fibrosing dermopathy can somewhat resemble scleroderma or scleromyxedema clinically, the face is typically spared in nephrogenic fibrosing dermopathy, unlike the other disorders, and paraproteinemia and autoantibodies are usually absent.