sclerocornea

sclerocornea

 [skle″ro-kor´ne-ah]
the sclera and cornea regarded as one.

scle·ro·cor·ne·a

(sklē'rō-kōr'nē-ă), [MIM*181700, MIM*269400]
1. The cornea and sclera regarded as forming together the hard outer coat of the eye, the fibrous tunic of the eye.
2. A congenital anomaly in which the whole or part of the cornea is opaque and resembles the sclera; other ocular abnormalities are frequently present.

scle·ro·cor·ne·a

(skler'ō-kōr'nē-ă)
1. The cornea and sclera regarded as forming together the hard outer coat of the eye, the fibrous tunic of the eye.
2. A congenital anomaly in which the whole or part of the cornea is opaque and resembles the sclera; other ocular abnormalities are frequently present.

sclerocornea 

A rare, congenital condition in which the sclera and cornea are considered as a single layer. The limbus is ill defined and portions of opaque scleral tissue with conjunctival vessels cover the cornea. The condition is usually bilateral and frequently associated with cornea plana. Visual acuity is reduced and often it is merely light perception if the entire cornea is involved. The eye is usually hyperopic. Systemic associations include mental retardation, deafness and craniofacial abnormalities. Treatment includes correction of the refractive error but in cases of central corneal opacification keratoplasty may be indicated.
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References in periodicals archive ?
Genetic eye disease spans developmental eye defects such as structural globe anomalies (microphthalmia, anophthalmia, ocular coloboma), anterior segment dysgenesis (including aniridia and sclerocornea), congenital cataracts, primary congenital glaucoma, congenital nystagmus, optic nerve disorders (ranging from hypoplasia to morning glory disc anomaly), to later childhood and adult-onset disorders including corneal and retinal dystrophies, and hereditary optic neuropathies.
Genomic medicine for inherited eye disease: This article provides a guide to the basics of genetic eye disease and how we are moving to the era of genomic medicine in ophthalmology
These included microcornea (2%), microcornea with iris coloboma (1%), sclerocornea (0.5%), iris coloboma (7%), aniridia (6.5%), ectopia lentis (4%), coloboma of lens (1%), anophthalmos (0.5%) and microphthalmos (1.5%).
Childhood ocular morbidity in Kumaon region--a tertiary hospital study
###* Persistent fetal vasculature (persistent###* Sclerocornea
PHACE syndrome: A case report
Ophthalmologic examination revealed bilateral microphthalmia, sclerocornea, iris and chorioretinal coloboma, blepharophimosis and dacryostenosis (Figure 1a,b).
A case with microphthalmia and multiple congenital anomalies/mikroftalmi ve coklu konjenital anomalili bir olgu
Other causes include birth trauma, prenatal infections, congenital corneal dystrophies, sclerocornea, metabolic storage diseases, interstitial keratitis, infective keratitis, Peter's anomaly and corneal scarring.
The paediatric ophthalmic examination: examination of a child's eye can be challenging and traumatic but could save the child's sight or even his life
Sclerocornea, hypertelorism, syndactyly, and ambiguous genitalia.
Case report: hypodontia and short roots in a child with Fraser syndrome
If the concern with clarity is a focal opacity that is peripherally located, think of congenital conditions such as dermoid and sclerocornea, or acquired causes such as bacterial keratitis, the presence of a foreign body, and band keratopathy.
What to ask when a child's eye 'looks funny"
Axenfeld-Reiger syndrome, Peters' anomaly, Alagille syndrome and Sclerocornea. Embryologically, posterior embryotoxon is one of the mesenchymal dysgenesis of the anterior ocular segment caused by the abnormal migration of neural crest cells.
Rare association of posterior embryotoxon with maxillary hypoplasia, ventricular septal defect, pulmonary atresia and patent ductus arteriosus
MIDAS###MIDAS syndrome(microphthalmia, dermal aplasia, and sclerocornea).9
Acronyms in dermatology literature; an appraisal

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