right ventricular dysplasia

Also found in: Acronyms.

arrhythmogenic right ventricular cardiomyopathy

A non-ischaemic right ventricular cardiomyopathy, which is the single most common cause of sudden cardiac death attributable to heredity. It presents in children and young (male) adults as syncope due to ventricular arrhythmia or as sudden cardiac death in young athletes.
Clinical findings Strong familial tendency; asymptomatic, 10%; recurrent ventricular tachycardia with left bundle branch pattern, 45%; congestive heart failure, 25%; heart murmur, 10%; sudden death, 5%. Usually presents with palpitations, syncope, symptomatic arrhythmias, or sudden death during exercise in a young person.
Diagnosis EKG T wave inversion in V1–V3; 2-D and M mode echocardiography may be useful.
Management Beta-blockers, ablation with 90% initial success rate but 60% recurrence, implantable cardioverter-defibrillators, treatment of heart failure when it develops.
Segen's Medical Dictionary. © 2012 Farlex, Inc. All rights reserved.

right ventricular dysplasia

Arrhythmogenic right ventricular dysplasia, right ventricular cardiomyopathy Cardiology An idiopathic form of right ventricular cardiomyopathy Clinical Strong familial tendency with variable infiltration or replacement of myocardium by fat and/or fibrous tissue Findings 10% are asymptomatic, recurrent ventricular tachycardia with left bundle branch pattern–45%, CHF–25%, heart murmur–10%, sudden death–5% Diagnosis T wave inversion in V1-V3 of the EKGl. See Apoptosis, Cardiomyopathy.
McGraw-Hill Concise Dictionary of Modern Medicine. © 2002 by The McGraw-Hill Companies, Inc.
References in periodicals archive ?
Fibro-adipose tissue was found in 7 of 42 hearts from autopsy (which did not have right ventricular dysplasia), with different distribution in the two ventricles, but to a maximum amount of 20% of the section.
Diagnosis of arrhythmogenic right ventricular dysplasia cardiomyopathy.
Among the other cases of SCA in this age group, 80% of patients with arrhythmogenic right ventricular dysplasia have ECG abnormalities, as do high proportions of patients with long-QT and Brugada syndromes and dilated cardiomyopathy [98,102-104].
* Some forms of cardiomyopathy, including hypertrophic cardiomyopathy, familial dilated cardiomyopathy, and arrhythmogenic right ventricular dysplasia.
A third type of known irregularity is arrhythmogenic right ventricular dysplasia (ARVD), in which fatty tissue has replaced normal heart muscle.
The third type is so rare that we don't discuss it much and the final type is arrhythmogenic right ventricular dysplasia, a rare disorder which damages the right side of the heart.
[ClickPress, Thu Jun 20 2019] By epidemiology, according to the Centers for Diseases Control and Prevention, arrhythmogenic right ventricular dysplasia has a prevalence of 1 in 2500 to 1 in 5000 population.
Citation: "Studying arrhythmogenie right ventricular dysplasia with patient-specific iPSCs"; Changsung Kim et al.; Nature, 2013, DOI: 10.1038/naturel1799, published online 27 January 2013
Uhl's anomaly, arrhythmogenic right ventricular dysplasia / cardiomyopathy (ARVD/C) and right ventricular outflow tract ventricular tachycardia (RVOT VT) involve pathogenic changes in the right ventricular (RV) myocardium.
Indication for Complete number sheath months extraction removal 1 14F 51 Pocket Yes infection 2 14F 58 Lead Yes dysfunction 3 12 F 25 Lead Yes fracture 4 14F 34 Pocket Yes infection Total Case extraction number time, minutes Complication 1 43 No 2 38 No 3 42 No 4 36 No ARVD- arrhythmogenic right ventricular dysplasia, CMP- cardiomyopathy, F- female, LLD- lead locking device, M- male, VT- ventricular tachycardia

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