retroperitoneal sarcoma

retroperitoneal sarcoma

A nonspecific term for any sarcoma arising in the retroperitoneal region, which comprises 15% of all sarcomas (of 8,600 cases/year, USA).
 
Clinical findings
Often asymptomatic abdominal mass; average age, 50.

Prognosis
65% to 80% of cases achieve complete resection; 5-year local recurrence, ±50%; 5-year survival, ±50%.

Histological types of retroperitoneal sarcoma
• Liposarcoma—41%;
• Leiomyosarcoma—28%;
• Malignant fibrous histiocytoma (MFH)—7%;
• Fibrosarcoma—6% (MFH and fibrosarcoma are now viewed as synonyms);
• Malignant peripheral nerve sheath tumour—3%.
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References in periodicals archive ?
Summary: Both patient and her kidney saved by operation on retroperitoneal sarcoma
Neoadjuvant radiotherapy for retroperitoneal sarcoma: a systematic review.
Carcinoma caecum and retroperitoneal sarcoma accounts for 4% of cases.
The Transatlantic Retroperitoneal Sarcoma Working Group (TARPSWG) has published on 1,007 primary RPS patients treated in eight North American and European sarcoma centers from 2002 to 2011 [8, 9].
Crago, "The importance of surgical margins in retroperitoneal sarcoma," Journal of Surgical Oncology, vol.
Hannay et al., "Outcome following resection of retroperitoneal sarcoma," British Journal of Surgery, vol.
Chakraborty, "Giant myelolipoma of left adrenal gland simulating a retroperitoneal sarcoma," International Journal of Advanced Medical and Health Research, vol.
Magnetic resonance imaging (MRI) of the pelvis followed and confirmed the solid nature of this mass, showing that it was independent from the bowel/rectum, featuring a retroperitoneal sarcoma type of mass rather than a lymph nodal bloc (Figure 1(b)).
Prognostic factors in retroperitoneal sarcoma: A multi-variateanalysis of a series of 165 patients of the French Cancer Center Federation Sarcoma Group.
Theoretically, the best option for retroperitoneal sarcoma is complete resection plus adjuvant therapy.
"The role of surgical margin status in retroperitoneal sarcoma," J Surg Oncol., 98, pp.607-610.
The most commonly encountered among the malignant mesenteric tumours are lymphomas followed by leiomyosarcoma.1 We present a case of huge mesenteric liposarcoma which was mistakenly labelled as a case of retroperitoneal sarcoma and the patient was being denied surgery for fear of irresectability due to its very large size.

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