Regional odontodysplasia (ROD) is uncommon developmental anomaly, which tends to be localised and involves the ectodermal and mesodermal tooth components .
Regional odontodysplasia typically affects one quadrant of the jaw, although it does occasionally cross the midline [7, 13-15]; however there are few cases where this anomaly has affected either the maxillary and mandibular quadrants of the same side [16, 17] or both quadrants of the same jaw [16, 18] and it is extremely rare for the anomaly to affect all four quadrants [13, 19].
The regional odontodysplasia, first reported in 1947, is a nonhereditary and rare dental developmental anomaly of unknown etiology (PORTELA; GONCALVES, 1988; ROSA et al., 2006; SANNOMIYA et al., 2002).
Both dentitions could be affected by the regional odontodysplasia (REDMAN et al., 1979) and it is more frequently found in maxilla than in mandible (PORTELA; GONCALVES, 1988), and on the anterior teeth (PANDIS et al., 1991; ZEGARELLI et al., 1963).
, also described as ghost teeth, has been described [for overview see Crawford and Aldred, 1989].
The list includes diabetes, chronic or cyclical loss of white blood cells, Papillon-Lefevre syndrome, Down syndrome, scurvy, dentin dysplasia, regional odontodysplasia
, Langerhans cell disease, leukemia, AIDS and hypophosphatasia.
is a rare developmental anomaly involving dental tissues.