Keywords: Anorectal malformation, colostomy, imperforate anus, posterior sagittal anorectoplasty, rectovestibular fistula
Then, a vertical incision was made through the layers from the lower end of the sacrum to the commisura posterior over the rectovestibular fistula.
We present such a case in a one-year-old female child with MRKH syndrome and rectovestibular fistula.
Keywords: Mayer-Rokitansky-Kuster-Hauser syndrome, atypical, rectovestibular fistula
Anorectal malformations are uncommonly reported to be associated with MRKH syndrome, and among them, rectovestibular fistula and cloacal malformations have been commonly described (1,2,6).
There is changing trend in the management of anorectal malformation with rectovestibular fistula as more patients with this condition are managed without a preliminary colostomy with good outcome.
advocated that operation on patients with rectovestibular fistula is safer under cover of a protective colostomy (8,7)
Primary anterior sagittal anorectoplasty for rectovestibular fistula.
Infantile vulvar abscess with a normal anus: a suspicious sign of rectovestibular fistula.
Transanal approach in repairing acquired rectovestibular fistula in females.
In intermediate anomalies, rectobulbar urethral fistula was the main anomaly noted in males, in females rectovestibular fistula was the commonest.
3 had rectal atresia Intermediate anomalies None Low anomalies 17 cases (6 membranous anus, 6 anocutaneous fistula, 5 anal stenosis) Female patients High anomalies None Intermediate anomalies 2 rectovestibular fistula Low anomalies 21 cases (5 ano cutaneous, 6 anal stenosis, 2 membranous anus, 8 anovestibular fistula) Cloaca / rare anomalies None Table 3: Comparative distribution of low anomalies Sex Anocuteneous Anal Membrane Anovestibular fistula stenosis anus fistula Present Males 15.