psammomatous melanotic schwannoma

psammomatous melanotic schwannoma

A rare tumour which usually occurs in the setting of Carney's complex, often seen in the gastrointestinal tract, most commonly in the stomach.
 
DiffDx
Melanoma, GIST, pigmented neuroendocrine tumor, epithelioid leiomyoma.
References in periodicals archive ?
Psammomatous melanotic schwannoma: a distinctive, heritable tumor with special associations, including cardiac myxoma and the Cushing syndrome.
Malignant psammomatous melanotic schwannoma of the spine: a component of Carney complex.
Psammomatous melanotic schwannoma localized in the mediastinum: diagnosis by fine-needle aspiration cytology.
Current discoveries and management of psammomatous melanotic schwannoma. J Cancer Tumor Int.
Intrathoracic psammomatous melanotic schwannoma associated with the Carney complex.
Psammomatous melanotic schwannoma. A distinctive, heritable tumor with special associations, including cardiac myxoma and the Cushing syndrome.
While nonpsammomatous MS is considered to be a sporadic type, encountered in fourth decades, psammomatous melanotic Schwannoma tends to occur at an earlier age (average age, 22.5 years).
Raque, "Malignant psammomatous melanotic schwannoma ofthe spine: A component of Carney complex," Surgical Neurology International, vol.
Huang, "Intrapulmonary psammomatous melanotic schwannoma," The Journal of Thoracic and Cardiovascular Surgery, vol.
Kaya, "Psammomatous melanotic schwannoma: a challenging histological diagnosis," Dermatopathology, vol.
The differential diagnoses include pigmented (melanotic) neurofibroma, psammomatous melanotic schwannoma, and desmoplastic (neurotrophic) melanoma.
Psammomatous melanotic schwannoma may present rarely as a colorectal polyp comprising epithelioid cells with psammoma bodies and melanin pigment.