primary systemic vasculitis

primary systemic vasculitis

A range of disorders of blood vessel walls featuring inflammation and cell death (necrosis) with thickening and nodular protrusions. The group includes polyarteritis nodosa, Wegener's granulomatosis, the CHURG-STRAUSS SYNDROME and KAWASAKI DISEASE.
References in periodicals archive ?
This cohort is part of the Diagnostic and Classification Criteria in Vasculitis Study (DCVAS), which aims to develop classification and diagnostic criteria for primary systemic vasculitis.
Biologic therapy in primary systemic vasculitis of the young.
Savage CO, Harper L, Adu D: Primary systemic vasculitis.