The most common etiology of hearing impairment was an idiopathic progressive postlingual hearing loss
The compound heterozygosity for a mild and severe mutations leads to postlingual hearing loss, whereas the combination of two severe mutations leads to profound hearing impairment with a prelingual onset .
Prelingual and postlingual hearing loss was classified according to the onset of prominent hearing loss.
Eggermann et al., "Autosomal recessive postlingual hearing loss (DFNB8): compound heterozygosity for two novel TMPRSS3 mutations in German siblings," Journal of Medical Genetics, vol.
Prelingual and postlingual hearing loss were classified by the onset age of prominent hearing loss.
Compound heterozygosity for a mild and severe mutation leads to postlingual hearing loss (DFNB8), whereas the combination of two severe mutations leads to profound hearing impairment with prelingual onset (DFNB10) .
Finally, we expected to see a difference in the progress of adaptation and the involvement of cortical areas between CI users with postlingual hearing loss and CI users with prelingual hearing loss.
Furthermore, the results showed a difference in the way CI recipients with postlingual hearing loss and recipients with prelingual hearing loss distinguish between speech and babble.