polycystic liver disease


Also found in: Acronyms, Wikipedia.

pol·y·cys·tic liv·'er

gradual cystic dilation of intralobular bile ducts (Meyenburg complexes) that fail to involute in embryologic development of the liver; frequently associated with bilateral congenital polycystic kidneys and occasionally with cystic involvement of the pancreas, lungs, and other organs.

polycystic liver disease

A condition characterized by multiple variably-sized cysts lined by cuboidal epithelium; liver disease is often obscured by accompanying adult polycystic kidney disease; 40% of affected livers also have von Meyenburg's complexes
References in periodicals archive ?
Laparoscopic surgery and polycystic liver disease: Clinicopathological features and new trends in management.
Medical and surgical treatment options for polycystic liver disease. Hepatology 2010;52:2223-30.
Taylor, "Management of polycystic liver disease," Current Fungal Infection Reports, vol.
Cantz et al., "Outcome and quality of life in patients with polycystic liver disease after liver or combined liver-kidney transplantation," Liver Transplantation, vol.
Portmann et al., "Hepatic venous outflow obstruction in patients with polycystic liver disease: pathogenesis and treatment," Gut, vol.
Treatment of symptomatic polycystic liver disease: Transcatheter super-selective hepatic arterial embolization using a mixture of NBCA and iodized oil.
Polycystic liver diseases (PLDs) represent a group of genetic disorders in which cysts occur in the liver (autosomal dominant PLD) or in combination with cysts in the kidneys (autosomal dominant polycystic kidney disease).[sup][1],[2] Most patients with PLD are asymptomatic and require no special treatment.
Cyst infection in autosomal dominant polycystic kidney disease/autosomal dominant polycystic liver disease (ADPLD) documented by several imaging methods (A-G) and histology (H-l).
Clinical manifestations at hospital admission in patients with autosomal dominant polycystic kidney disease/autosomal dominant polycystic liver disease with kidney and/or liver cyst infections.
(10) Peribiliary cysts are associated with advanced and portal hypertensive liver disease and are also present in patients with polycystic liver disease. (11) Uncommon complications of peribiliary cysts include obstructive jaundice and hepatolithiasis.
Polycystic liver diseases: Congenital disorders of cholangiocyte signaling.
Autosomal dominant polycystic liver disease is part of the spectrum of fibropolycystic liver diseases that are caused by congenital bile duct malformation, including bile duct hamartoma, Caroli's disease, congenital hepatic fibrosis, and choledochal cyst.

Full browser ?