Intense pulsed light works well in patients with both pigmentary and vascular changes, especially for poikiloderma
with brown and red pigment.
The patient was emaciation, and physical examination revealed heliotrope sign, poikiloderma
involving the face, “V” sign of the chest, and the upper arm, nail fold telangiectasia, and large well-defined ulcers on the abdomen, back, and upper arms, there was no Gottron sign [Figure 1].
Kindler syndrome (KS) is a rare autosomal recessive genetic disorder presenting as progressive dermatoses, skin blisters, poikiloderma
, pigmentation, and photosensitivity.
A benign condition, poikiloderma
of Civatte typically affects the sides of the neck, as you describe, although it may also appear on the sides of the face or on the upper chest.
, and episodic angioedema can also occur.
10) reported a case of a 38 year old male patient who presented with generalised erythema, scaling and poikiloderma
, with multiple nodulo-ulcerative lesions for 2 years, suggestive of lepromatous leprosy.
7 Clinically DKC is characterized by a triad of reticulate pigmentation of the skin resembling poikiloderma
atrophicans vasculare, nail dystrophy with failure of the nails to form a nail plate and leucokeratosis of the oral mucosa.
Less specific, but not uncommon skin manifestations include poikiloderma
, seborrhoeic dermatitis/psoriasiform changes of the scalp and diffuse erythroderma.
33% cases were of actinic lichen planus, drug induced lichenoid eruption, and poikiloderma
, hypertropic lichen planus, eruptive lichen planus & lichen spinulosus each had 2.
Poikilodermatous mycosis fungoides is a rare distinct clinical variant of cutaneous T-cell lymphoma (CTCL), formerly referred to as poikiloderma
vasculare atrophicans or parapsoriasis variegata.
Unlike EAC, these rings do not show a trailing scale and the patches may demonstrate poikiloderma
(erythema, atrophy, and dyspigmentation).
The first most frequent sign is poikiloderma
in addition to sparse scalp hair and eyelashesshort statusskeletal abnormalities juvenile cataract and premature aging.