pigmented neuroectodermal tumor of infancy
pigmented neuroectodermal tumor of infancyA tumor of neural crest origin affecting infants < 6 months of age, seen in the anterior maxilla, oral cavity and skull, less commonly in the mediastinum, thigh, forearm, epididymis Clinical Locally aggressive, 15% recur; few metastasize Lab ↑ VMA in urine. See Pseudonym syndrome.
McGraw-Hill Concise Dictionary of Modern Medicine. © 2002 by The McGraw-Hill Companies, Inc.