phosphaturic mesenchymal tumour

phosphaturic mesenchymal tumour

A rare and very small mesenchymal tumour that causes osteomalacia by secreting a phosphaturic hormone—fibroblast growth factor-23/FGF-23. Most are termed phosphaturic mesenchymal tumours, mixed connective tissue type, and occur in middle-aged adults, either in soft tissue or bone.

Management
Excision reduces phosphate wasting and osteomalacia.
References in periodicals archive ?
INTRODUCTION: Phosphaturic mesenchymal tumour is a cause of tumour induced osteomalasia (TIO) which is a well-known para neoplastic association.
DISCUSSION: Phosphaturic mesenchymal tumour is a rare soft tissue neoplasm that most commonly presents as osteomalacia.
Phosphaturic mesenchymal tumour of the sinonasal area: case report and review of the literature.