PEComa

(redirected from perivascular epithelioid cell tumour)

PEComa

A group of mesenchymal tumors composed of epithelioid and spindle cells displaying perivascular epithelioid (PEC) differentiation. The PEComa family of tumors includes angiomyolipoma, clear-cell "sugar" tumor of lung and gastrointestinal tract and other sites, lymphangioleimyomatosis, clear-cell myomelanocytic tumor of the falciform ligament.

PEComa

A rare, possibly mesenchymal tumour of unknown origin and of uncertain malignant potential, which can arise anywhere in the body and more commonly affects females.
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3) In recent years there have also been at least 8 reported cases of perivascular epithelioid cell tumour (PEComa) of the bladder.
Constant allelic alteration on chromosome 16p (TSC2 gene) in perivascular epithelioid cell tumour (PEComa): genetic evidence for the relationship of PEComa with angiomyolipoma.
Malignant perivascular epithelioid cell tumour ("PEComa") of soft tissue: a unique case.
Cutaneous clear cell myomelanocytic tumour: a new member of the growing family of perivascular epithelioid cell tumours (PEComas): clinicopathological and immunohistochemical analysis of seven cases.