Perivascular epithelioid cell tumour | definition of perivascular epithelioid cell tumour by Medical dictionary
PEComa (redirected from perivascular epithelioid cell tumour)
A group of mesenchymal tumors composed of epithelioid and spindle cells displaying perivascular epithelioid (PEC) differentiation. The PEComa family of tumors includes angiomyolipoma, clear-cell "sugar" tumor of lung and gastrointestinal tract and other sites, lymphangioleimyomatosis, clear-cell myomelanocytic tumor of the falciform ligament.
PEComa A rare, possibly mesenchymal tumour of unknown origin and of uncertain malignant potential, which can arise anywhere in the body and more commonly affects females.
References in periodicals archive
3) In recent years there have also been at least 8 reported cases of perivascular epithelioid cell tumour
(PEComa) of the bladder.
Constant allelic alteration on chromosome 16p (TSC2 gene) in perivascular epithelioid cell tumour
(PEComa): genetic evidence for the relationship of PEComa with angiomyolipoma.
Malignant perivascular epithelioid cell tumour
("PEComa") of soft tissue: a unique case.
Cutaneous clear cell myomelanocytic tumour: a new member of the growing family of perivascular epithelioid cell tumours
(PEComas): clinicopathological and immunohistochemical analysis of seven cases.