periodic polyserositis
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fa·mil·i·al par·ox·ys·mal pol·y·ser·o·si·tis
[MIM*249100]transient recurring attacks of abdominal pain, fever, pleurisy, arthritis, and rash; the condition is asymptomatic between attacks; autosomal recessive inheritance, caused by mutation in the marenostrin gene on 16p. There is an autosomal dominant form [MIM*134610] in which amyloidosis is common.
Synonym(s): benign paroxysmal peritonitis, familial Mediterranean fever, familial recurrent polyserositis, Mediterranean fever (2) , periodic peritonitis, periodic polyserositis
Farlex Partner Medical Dictionary © Farlex 2012
periodic polyserositis
(1) A nonspecific term for any recurring inflammation of serous membranes.(2) Familial Mediterranean fever (see there), OMIM:249100.
Segen's Medical Dictionary. © 2012 Farlex, Inc. All rights reserved.