International periodic fever
, aphthous stomatitis, pharyngitis, cervical adenitis syndrome cohort: description of distinct phenotypes in 301 patients.
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syndrome," Blood, vol.
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, aphthous stomatitis, pharyngitis, and adenopathy syndrome in comparison with the typical pediatric expression of disease," Mediators of Inflammation, vol.
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Syndromes are a group of diseases that cause serious recurrent fever and pathogenic inflammation through non-infectious activation of the immune system.
Clinical immunology review series: An approach to the patient with a periodic fever
The Breakthrough Designations were granted based on the Phase III trial ("Canakinumab Pivotal UmbreUa Study in Three Hereditary Periodic Fevers
 Kyvsgaard N, Mikkelsen T, Korsholm J, Veirum JE, Herlin T Periodic fever
associated with aphthous stomatitis, pharyngitis and cervical adenitis.
Unlike a fever of unknown origin, recurrent and periodic fevers
occur regularly in repeated cycles or intermittently over a period of time.
Autoinflammatory disorders: a new concept in hereditary periodic fever
Familial Mediterranean fever and related periodic fever
syndromes/ autoinflammatory diseases.