Anterolateral thigh fasciocutaneous island flaps in
perineoscrotal reconstruction.
An autosomal recessive male DSD, termed pseudovaginal
perineoscrotal hypospadias, was described in 1961 by Nowakowski and Lenz.
On physical examination, he had a phallus-like structure of 1.5 cm,
perineoscrotal hypospadias, a perineal blind vaginal pouch and posterior labioscrotal fusion (Figure 1).
Lastly, other syndromes and conditions with genital abnormalities, such as cloacal exstrophy of the bladder (multi-organ pelvic defect resulting in severe inadequacy or absence of genitalia),
perineoscrotal hypospadias, micropenis, penile agenesis (aphallia), vaginal agenesis, and penile ablation (loss of penis from traumatic injury), are blanketed by the phrase DSD.
The occurrence of
perineoscrotal or perineal hypospadias is 20% and the incidence of complete penoscrotal trans position is lower and may be associated with other renal anomalies, like renal agenesis.
De L'hypospadias
perineoscrotal et de son traitement chirurgical.
In these cases there is no option but to perform a substitution urethroplasty using a
perineoscrotal fasciocutaneous flap.
In the present study we used the
perineoscrotal junction as the anterior landmark to measure the distance from the anus.
Ambiguous genitalia with
perineoscrotal hypospadias in 46, XY individuals: Long-term medical, surgical, and psychosexual outcome.
Yu et al.[7] used the anterolateral thigh fasciocutaneous island flap in
perineoscrotal reconstruction.
In India, a patient with
perineoscrotal hypospadias and micropenis was observed to have a novel heterozygous missense mutation Q56H and V89L homozygous polymorphism (19).
Perineoscrotal reconstruction using a medial circumflex femoral artery perforator flap.
