osteofibrous dysplasia


Also found in: Dictionary, Thesaurus, Encyclopedia.

osteofibrous dysplasia

(os'tē-ō-fī'brŭs dis-plā'zē-ă),
fibroosseous intracortical lesion that occurs almost exclusively in tibias and fibulas of children.

osteofibrous dysplasia

A rare, self-limiting non-neoplastic lesion which usually arises in the cortex of the tibia and fibula, or both, most often in the middle third of the diaphysis, affecting children < age 15.
 
Clinical findings
Pain, pathological fracture, swelling, deformity; may be asymptomatic for up to 5 years.

Imaging
Well-defined intramedullary lytic lesion with a sclerotic rim; the cortex often is expanded and thinned, with multiple radiolucencies admixed with intervening areas of sclerosis.

osteofibrous dysplasia

An extremely rare, benign bone tumor occurring in children under 10. The primary symptoms are painless swelling or bowing of bone. It usually develops in the tibia or fibula.
See also: dysplasia
References in periodicals archive ?
Cytokeratin expression and distribution in adamantinoma of the long bones and osteofibrous dysplasia of tibia and fibula: an immunohistochemical study correlated to histogenesis.
Morphologic diversity of long bone adamantinoma: the concept of differentiated (regressing) adamantinoma and its relationship to osteofibrous dysplasia.
Adamantinoma, osteofibrous dysplasia and differentiated adamantinoma.