ornithine carbamoyltransferase


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Related to ornithine carbamoyltransferase: ornithine carbamoyltransferase deficiency

ornithine

 [or´nĭ-thēn]
an amino acid obtained from arginine by splitting of urea; it is an intermediate in urea biosynthesis.
ornithine carbamoyltransferase (ornithine transcarbamylase) an enzyme that catalyzes a reaction occurring in the liver mitochondria as part of the urea cycle.

or·ni·thine car·bam·o·yl·trans·fer·ase

an enzyme catalyzing formation of l-citrulline and orthophosphate from l-ornithine and carbamoyl phosphate; a part of the urea cycle; a deficiency of this enzyme will result in ammonia intoxication and impaired urea formation.
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