Other dermatoses observed in this study were Lichen striatus, Linear Lichen planus, inflammatory Linear verrucous epidermal nevus, Lichen nitidus, Paederus dermatitis, Hypomelanosis of Ito, Linear and Whorled nevoid
Segmental lent ginosis within nevoid
(2-4) However, no one has reported an FR of the tongue in a patient with nevoid
basal cell carcinoma syndrome (NBCCS).
Gene: PTCH1 Chromosome: 9q22.32 Mode of inheritance: Autosomal dominant Syndrome: Nevoid
basal cell carcinoma syndrome/Gorlin syndrome
basal cell carcinoma (Gorlin's) syndrome (NBCCS) is an autosomal-dominant disorder that is caused by a mutation of both alleles of the PTCH gene.
psoriasis probably reflects mosaicism for a gene responsible for psoriasis.
The gene associated with nevoid
basal cell carcinoma syndrome is known to have a tumor suppressor function and to be related to the PTCH gene.
It can be a feature of Gorlin--Goltz syndrome, a multisystem disorder that manifest with multiple Nevoid
basal cell carcinoma, jaw cysts, congenital skeletal abnormalities such as bifid, splayed or synostotic ribs.
Blaschko's lines (BL) are the surface patterns manifest by various nevoid
and acquired skin diseases on the human skin and mucosa.
Basal cell nevus syndrome or nevoid
basal cell carcinoma syndrome (BCNS; Gorlin syndrome) is a rare autosomal, dominantly inherited condition with variable expressivity, although 30% to 50% of cases are due to spontaneous mutations.
Linear and whorled nevoid
hypermelanosis associated with developmental delay and generalized convulsions.
INTRODUCTION: Linear and whorled nevoid
hypermelanosis (LWNH) was first described by Kalter et al (1) in 1988 as a sporadic pigmentary anomaly characterized by swirls and streaks of macular(flat) hyperpigmentation following the lines of Blaschko.Usually occurring as isolated disorder of pigmentation, associated chromosomal abnormalities with central nervous, cardiovascular, musculoskeletal and ocular abnormalities have been reported.