PEComa

(redirected from monotypic epithelioid angiomyolipoma)

PEComa

A group of mesenchymal tumors composed of epithelioid and spindle cells displaying perivascular epithelioid (PEC) differentiation. The PEComa family of tumors includes angiomyolipoma, clear-cell "sugar" tumor of lung and gastrointestinal tract and other sites, lymphangioleimyomatosis, clear-cell myomelanocytic tumor of the falciform ligament.
Synonym(s): extrapulmonary sugar tumor, monotypic epithelioid angiomyolipoma, perivascular epithelioid cell tumor

PEComa

A rare, possibly mesenchymal tumour of unknown origin and of uncertain malignant potential, which can arise anywhere in the body and more commonly affects females.
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References in periodicals archive ?
Primary monotypic epithelioid angiomyolipoma of bone.
Epithelioid Angiomyolipoma: a morphologically distinct variant that mimics a variety of intra-abdominal neoplasms
Carcinoma like monotypic epithelioid angiomyolipoma in patients without evidence of tuberous sclerosis: a clinicopathologic and genetic study.
Molecular pathology of lymphangioleiomyomatosis and other perivascular epithelioid cell tumors
Carcinoma-like monotypic epithelioid angiomyolipoma in patients without evidence of tuberous sclerosis: a clinicopathologic and genetic study.
Oncocytoma-like angiomyolipoma: a clinicopathologic and immunohistochemical study of 2 cases. (Case Reports)

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