PEComa(redirected from monotypic epithelioid angiomyolipoma)
A group of mesenchymal tumors composed of epithelioid and spindle cells displaying perivascular epithelioid (PEC) differentiation. The PEComa family of tumors includes angiomyolipoma, clear-cell "sugar" tumor of lung and gastrointestinal tract and other sites, lymphangioleimyomatosis, clear-cell myomelanocytic tumor of the falciform ligament.
Synonym(s): extrapulmonary sugar tumor, monotypic epithelioid angiomyolipoma, perivascular epithelioid cell tumor
Farlex Partner Medical Dictionary © Farlex 2012
PEComaA rare, possibly mesenchymal tumour of unknown origin and of uncertain malignant potential, which can arise anywhere in the body and more commonly affects females.
Segen's Medical Dictionary. © 2012 Farlex, Inc. All rights reserved.