membranous lipodystrophy

mem·bra·nous lip·o·dys·tro·phy

a rare metabolic disease in which bone marrow fat cells are transformed into thick convoluted PAS-staining membranes enclosing weakly osmophilic material; leads to progressive cystic resorption of limb bones and dementia with sudanophilic leukodystrophy.

Nasu,

T., Japanese pathologist, 1915-1996.
Nasu disease - autosomal recessive disorder characterized by lipodystrophy, sclerosing leukoencephalopathy, and skeletal abnormalities. Synonym(s): membranous lipodystrophy; Nasu-Hakola disease
Nasu-Hakola disease - Synonym(s): Nasu disease
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