Megacystis, or dilated urinary bladder, includes causes of bladder outlet obstruction due to posterior urethral valves (PUV) and less commonly Prune Belly syndrome, Megacystis-Megaureter syndrome, megacystis-microcolon intestinal hypoperistalsis syndrome (MMIHS), anterior urethral valves, megalourethra
, urethral atresia and cloacal anomalies.
Megalourethra is a rare congenital urethral abnormality characterized by dilatation of the anterior urethra without any distal obstruction.
Here, we report a case of type IIA1 complete UD with megalourethra in both urethras.
Both the UD and the megalourethra are rare urethral anomalies and the concomitance of these two anomalies has not been reported previously.
Megalourethra is a rare congenital urethral anomaly that results from defective development of the corpus spongiosum alone or with hypoplastic corpora cavernosa that occurs in scaphoid or fusiform form, respectively.
Onlay Tubularised Island Island Flap (27) Flap (18) Complications No (%) No (%) Fistula 6 (22.2) 3 (16.6) Stricture 0 4 (22.2) Flap Necrosis 0 1 (5.5) Torsion 1 (3.7) 0 Recurrent Chordee 0 0 Megalourethra
0 0 Overall 7 (25.9) 8 (44.4) All UCFs underwent fistula repair 6 months post primary surgery and are doing fine.
Contraindications to neonatal circumcision include prematurity, family history of bleeding disorder, hypospadias/epispadias, webbed penis, micropenis, megalourethra
, ambiguous genitalia, bilateral large hydroceles, buried/concealed penis, and congenital penile lymphedema.
Megalourethra is a very rare congenital anomaly of penile urethra.
Key words: Infection; megalourethra; urinary anomaly.
Pathogenesis of megalourethra. J Urol 1993;149:1512-6.
Males born with penile anomalies (hypospadias, epispadias or megalourethra
) and children with ammonia dermatitis were excluded from the study.