medulloepithelioma


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medulloepithelioma

 [mĕ-dul″o-ep″ĭ-the″le-o´mah]
a brain tumor composed of primitive neuroepithelial cells lining the tubular spaces.

me·dul·lo·ep·i·the·li·o·ma

(med'yū-lō-ep'i-thē'lē-ō'mă),
A rare, primitive, rapidly growing intracranial neoplasm thought to originate from the cells of the embryonic medullary canal and hence included with ependymoblastomas by some neuropathologists; ganglion cells and astrocyte maturation have also been reported. Tumors that occur in the ciliary body are referred to as embryonal medulloepitheliomas.
[medullo- + epithelium + -oma, tumor]

medulloepithelioma

A highly aggressive, undifferentiated primitive neuroepithelial tumour of small children (up to age 5), which may contain bone, cartilage, and skeletal muscle; it tends to metastasise extracranially.

Medulloepithelioma of the eye arises in the ciliary epithelium; it is known as diktyoma or embryonal medulloepithelioma.

medulloepithelioma

A highly malignant undifferentiated primitive neuroepithelial tumor of children that may contain bone, cartilage, skeletal muscle; it tends to metastasize extracranially; MEs of the eye arise in the ciliary epithelium, and are termed diktyomas

me·dul·lo·ep·i·the·li·o·ma

(mĕ-dŭl'ō-ep'i-thē'lē-ō'mă)
A rare, primitive, rapidly growing intracranial neoplasm thought to originate from the cells of the embryonic medullary canal.
[medullo- + epithelium + -oma, tumor]

medulloepithelioma

1. A rare eye tumour affecting the CILIARY BODY or RETINA. May be BENIGN or MALIGNANT. Also known as dictyoma.
2. A rare malignant tumour of the nervous system.
References in periodicals archive ?
Key Words: Spectrum, glioma, meningioma, neurofibroma, medulloblastoma, medulloepithelioma, craniopharyngioma, paraganglioma.
Embryonal tumor with abundant neuropil and true rosettes (ETANTR), ependymoblastoma, and medulloepithelioma share molecular similarity and comprise a single clinicopathological entity.
An intraocular mass excision biopsy was performed, and the pathology demonstrated it was a ciliary body medulloepithelioma of the left eye.
Medulloepithelioma is occasionally a mimicker of uveitis in adults [14], but ultrasound may assist in the diagnosis as medulloepithelioma typically shows a mass with cystic spaces.
Reported medulloepithelioma cases describe a rapidly expanding ciliary body mass that masqueraded as chronic uveitis, cataract, and uncontrolled secondary glaucoma [27].
Immunohistochemical characterization of a malignant intraocular teratoid medulloepithelioma in a cockatiel.
(1) Medulloepithelioma is another primary intraocular tumor of childhood that arises in the ciliary epithelium and may contain small round blue cells similar in histologic appearance to retinoblastoma.
Results: Fine-needle aspiration biopsy of 14 patients showed that 3 had optic nerve melanocytoma, 2 had chorodial melanoma, 1 had iridociliary medulloepithelioma, 1 had iris melanoma, 1 had trabecular meshwork melanoma, 1 had iris nevus, 1 had leukemic infiltration, 1 had lymphoma, 1 had neuroendocrine carcinoma,!
Intraocular medulloepithelioma is a congenital tumor of the nonpigmented ciliary epithelium, usually diagnosed in childhood.
(118,119) These are typically pediatric tumors and include medulloblastoma, supratentorial "central" PNET, medulloepithelioma, ependymoblastoma, and atypical teratoid rhabdoid tumor (AT/RT).
A variety of melanotic brain tumors have been described in the literature, including ependymoma, choroid plexus papilloma and carcinoma, medulloblastoma, medulloepithelioma, schwannoma, meningioma, melanocytoma, and melanoma.
Evidence of neuronal and glial differentiation may be present.[1-6] Differentiation into specific mesenchymal tissues, such as cartilage, bone, skeletal muscle, smooth muscle, or adipose tissue in these embryonal tumors, is rare and has been reported in a few cases of medulloblastoma,[7-12] a cerebral medulloepithelioma,[13] and a case of cerebral PNET.[14] Herein, we report a PNET of the occipital lobe that showed extensive adipose tissue and glial differentiation.