malignant solitary fibrous tumour

malignant solitary fibrous tumour

An uncommon soft tissue malignancy (66% to 90% of SFTs are benign), most of which arise in the pleura. Extrapleural SFTs are even rarer, with about 100 having been reported in the world literature, arising in the meninges, orbit, upper respiratory tract, salivary glands, thyroid, peritoneum, liver, retroperitoneum, adrenal gland, kidney, spermatic cord, urinary bladder and prostate spinal cord, periosteum and soft tissue, mainly in the head and neck.
 
DiffDx
Haemangiopericytoma, synovial sarcoma, dermatofibrosarcoma protuberans, leiomyosarcoma, liposarcoma, malignant peripheral nerve sheath tumour.

Management
Excision, radiation therapy.
References in periodicals archive ?
Cytokeratin-positive malignant solitary fibrous tumour of the pleura: an unusual pitfall in the diagnosis of pleural spindle cell neoplasms.
Radical resection of a giant, invasive and symptomatic malignant Solitary Fibrous Tumour (SFT) of the pleura.
Histologically malignant solitary fibrous tumour of the anterior thoracic wall: a case report and review of the literature.
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