28) Rarely, median nerve lipomatosis (fibrolipomatous hamartoma) is detected in the investigation of macrodystrophia lipomatosa
or carpal tunnel syndrome.
; macrodactyly related to affected nerves, and a rewiew of literature.
Macrodystrophia lipomatosa (MDL) results from progressive overgrowth of all the mesenchymal elements, with a disproportionate increase in fibro-adipose tissue.
Macrodystrophia lipomatosa was first described by Feriz in 1925 and is a rare cause of focal gigantism by deposition of fat in the soft tissue of one or more digits of the hand or foot in association with hypertrophy of the phalanges and affected limbs.
Macrodystrophia Lipomatosa with associated fibrolipomatous hamartoma of the median nerve.
Macrodystrophia lipomatosa - a rare congenital disorder.
Blackskin M, Barnes FJ, Lyons MM: MR diagnosis of macrodystrophia lipomatosa.
(MDL) results from progressive overgrowth of all the mesenchymal elements with a disproportionate increase in the fibro-adipose tissues.
(MDL) is described as a rare, non-hereditary, congenital condition presenting with localised macrodactyly and a proliferation of mesenchymal elements.
is a rare congenital disorder of focal gigantism affecting the extremities, more commonly the second and third digits of the foot, but it may also affect the hand.
is a form of lipofibromatosis without bony overgrowth.