lymphangioleiomyomatosis


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lymphangiomyomatosis

 [lim-fan″je-o-mi″o-mah-to´sis]
a progressive disorder of women of child-bearing age, marked by nodular and diffuse interstitial proliferation of smooth muscle in the lungs, lymph nodes, and thoracic duct. Called also lymphangioleiomyomatosis.

lym·phan·gi·o·lei·o·my·o·ma·to·sis

(lim-fam'jē-ō-lī'ō-nū'ō-mă-tō'sis), [MIM*606690]
A rare disorder of unknown etiology seen in women of reproductive age and in patients of either sex with tuberous sclerosis. Pulmonary complications are due to hamartomatous proliferation of smooth muscle cells preferentially along bronchovascular structures resulting in obliteration of the airways and consecutive development of cysts in the lungs. Usually progressive, leading to death from respiratory failure. Treatment by lung transplantation has been successful.

lymphangioleiomyomatosis

/lym·phan·gio·leio·myo·ma·to·sis/ (lim-fan″je-o-li″o-mi″o-mah-to´sis) lymphangiomyomatosis.
References in periodicals archive ?
Klein, "Nephron-sparing nephrectomy for giant renal angiomyolipoma associated with lymphangioleiomyomatosis," Urology, vol.
Everolimus for angiomyolipoma associated with tuberous sclerosis complex or sporadic lymphangioleiomyomatosis (EXIST-2): A multicentre, randomised, double-blind, placebo-controlled trial.
Science company Pfizer (NYSE:PFE) revealed on Friday the receipt of the US Food and Drug Administration's (FDA) approval for RAPAMUNE (sirolimus) for the treatment of lymphangioleiomyomatosis (LAM), a rare, progressive disease that affects the lungs, kidneys and the lymphatic system.
A snapshot of the global therapeutic scenario for Lymphangioleiomyomatosis.
Rare DPLD with Lymphangioleiomyomatosis (LAM) well-defined features Langerhans' cell histiocytosis (LCH) 4.
2010) and a potentially devastating lung condition called lymphangioleiomyomatosis (LAM; Bissler et al.
Among the many community and professional organizations with which McKenna is deeply involved are Meals on Wheels for WNY; the Junior League of Buffalo; the WNY Friends of the LAM Foundation, which raises funds for, and awareness of, lymphangioleiomyomatosis (LAM), a progressive lung disease for which there's currently no cure; and the Public Relations Society of America.
The text opens with an historical overview, followed by physiological and radiological features of common ILDs, such as idiopathic interstitial pneumonia, non-specific interstitial pneumonitis, and sarcoidosis, and uncommon ILDs, such as lymphangioleiomyomatosis, Langerhans cell granulomatosis, drug-induced lung disease, eosinophilic lung disease, alveolar proteinosis, and alveolar michrolithiasis.
Pulmonary lymphangioleiomyomatosis (LAM) is a rare disease affecting fertile women and is characterized by progressive dyspnea on exertion.
The charity supports women with lymphangioleiomyomatosis.
7 Lung involvement may present with a clinical picture of lymphangioleiomyomatosis and pneumothorax.
Lymphangioleiomyomatosis (LAM) is pronounced "lim-fan je-o-liomi o-ma-to sis", a rare lung disease that was first discovered in 1918 and then written about by Von Stossel in 1937.