long-chain/very long-chain acyl-CoA dehydrogenase deficiency

(redirected from long-chainvery long-chain acyl-CoA dehydrogenase deficiency)

long-chain/very long-chain acyl-CoA dehydrogenase deficiency

a disorder of fatty acid oxidation in patients who lack the enzyme very long chain acyl-CoA dehydrogenase; sometimes manifested as weakness, hypotonia, cardiomyopathy, rhabdomyolysis, and episodes of hypoglycemia during fasting.
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