long-chain/very long-chain acyl-CoA dehydrogenase deficiency
(redirected from long-chainvery long-chain acyl-CoA dehydrogenase deficiency)long-chain/very long-chain acyl-CoA dehydrogenase deficiency
a disorder of fatty acid oxidation in patients who lack the enzyme very long chain acyl-CoA dehydrogenase; sometimes manifested as weakness, hypotonia, cardiomyopathy, rhabdomyolysis, and episodes of hypoglycemia during fasting.