keratolysis exfoliativa congenita

keratolysis exfoliativa congenita

superficial exfoliative dermatosis of the palms and soles. It starts as pinhead-sized white spots that gradually extend peripherally, forming anular thin scales, in the absences of inflammation.

Synonym(s): lamellar dyshidrosis, recurrent palmar peeling

A rare autosomal recessive form of congenital, ichthyosis characterised by peeling of skin, erythema, pruritus, short stature, eosinophilia, increased IgE