isovaleric acid


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i·so·va·ler·ic ac·id

(ī'so-vă-ler'ik as'id, -lēr'ik),
3-Methylbutyric acid; a metabolic intermediate in oxidative processes; elevated in cases of isovaleric acidemia.

isovaleric acid

/iso·va·ler·ic ac·id/ (i″so-vah-ler´ik) a carboxylic acid occurring in excess in the plasma and urine in isovalericacidemia.

isovaleric acid

[-vəler′ik]
Etymology: Gk, isos + L, valeriana, herb, acidus, sour
a fatty acid with a pungent taste and disagreeable odor that is found in valerian and other plant products, as well as in cheese. It also occurs as a metabolite of the amino acid leucine and is found in the sweat of feet and in the urine of patients with smallpox, hepatitis, and typhus. It has been used commercially in a variety of drugs, perfumes, and flavorings. Isovaleric acidemia occurs in patients who have abnormally high levels of isovaleric acid in the blood and urine as a result of an inherited deficiency of the enzyme isovaleryl coenzyme A dehydrogenase. The condition is treated with diets that contain low-leucine foods. Also called isopentoic acid, isopropylacetic acid.
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D Aliyu and Nwabueze (2007) synthesis and solution studies of coppor (11) valeric and isovaleric acid hydrazide in aqueous, medium J.
Synthesis and studies on the complexes of aceto and acetyladehyde: Valeric and Isovaleric acids hydrazones with Fe(II) and Co(II) sulphates
The basic oil components were isovaleric acid (0-2.
Variation in the composition of the essential oil of Valeriana officinalis L. roots from Estonia/Eeterliku oli koostise varieeruvus Eestist parineva Valeriana officinalis L. juurtes
Prior studies by others had awarded that distinction to steroids and isovaleric acid.
Armpit odor gets a chemical face
Characterizing the antifungal effects of isovaleric acid.
Student presentation awards at the 123[rd] meeting of the tennessee academy of science
Isovaleric acidemia (IVA) [4] (OMIM #243500) is caused by a defect in leucine catabolism due to deficiency of isovaleryl-coenzyme A (CoA) dehydrogenase, leading to the accumulation of free isovaleric acid, 3-hydroxyisovaleric acid, N-isovalerylglycine, and isovalerylcarnitine (C5).
Newborn screening for isovaleric acidemia using tandem mass spectrometry: data from 1.6 million newborns
When leucine is not used properly, it builds up as isovaleric acid and other harmful substances in the blood and urine that are toxic or poisonous.
Isovaleric acidemia
Isovaleric acid gets credit for the rancid and horsy elements.
Brett: when sanitation meets wine style
5%), bButyric acid (99%), isobutyric acid (99%), valeric acid (99%), isovaleric acid (99%), indole (99%), skatole (98%) and p-cresol (99%).
Characterization of odorant compounds from mechanical aerated pile composting and static aerated pile composting
Racial and cross-cultural differences have been reported for isovaleric acid (1.
World of flavor: ethnic taste preferences and wine
The alfalfa hay/ grain diet produced significantly higher pH, acetic, propionic and isovaleric acid concentrations when compared to the bromegrass hay diet.
THE EFFECTS OF DIET ON VOLATILE FATTY ACID CONCENTRATIONS IN THE STOMACH OF THE HORSE: IMPLICATIONS IN GASTRIC ULCER DISEASE
Valeric and isovaleric acid concentrations with yeast treatment were higher than that in control solutions at 8, 12, and 24 h (p<0.
Effects of Candida norvegensis live cells on in vitro oat straw rumen fermentation

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