insulin-dependent diabetes mellitus type 19
insulin-dependent diabetes mellitus type 19A multifactorial disorder of glucose homeostasis (OMIM:610155) characterised by susceptibility to ketoacidosis in the absence of insulin therapy.
Polydipsia, polyphagia, polyuria due to hyperglycaemia-induced osmotic diuresis and secondary thirst. Long-term diabetic complications affect the eyes, kidneys, nerves and blood vessels.
Defects of IFIH1, which encodes an RNA helicase, cause IDDM19.