incontinentia pigmenti achromians

hy·po·mel·a·no·sis of I·to

[MIM*146150, MIM*308300, MIM*300337]
not a specific entity but rather represents features of many different forms of mosaicism; characterized by unilateral or bilateral hypopigmented macules in whorls, streaks, and patches in a "marble-cake" pattern, variably associated with epidermal nevi, alopecia, and ocular, skeletal, and neural abnormalities.
See also: incontinentia pigmenti.

incontinentia pigmenti achromians

a congenital neurocutaneous syndrome, not present at birth but appearing in early life, characterized by the presence of peculiar whorled, linear, and splatter-like patterns of hypopigmentation and often associated with other abnormalities, including hair loss and ocular, musculoskeletal, and mental disturbances. It is unrelated to incontinentia pigmenti. Also called hypomelanosis of Ito.

Ito,

Minor, Japanese dermatologist, 1884-1982.
hypomelanosis of Ito - inherited hypopigmented macules variably associated with epidermal nevi, alopecia, and ocular, skeletal, and neural abnormalities. Synonym(s): incontinentia pigmenti achromians
Ito nevus - pigmentation of skin innervated by lateral branches of the supraclavicular nerve and the lateral cutaneous nerve of the arm.
References in periodicals archive ?
1,2) According to the literature, it has also been associated with some systemic conditions such as Mohr syndrome (Orofacial-digital talon cusp) (9), Sturge-weber syndrome (10), Rubinstein-Taybi syndrome (11), incontinentia pigmenti achromians and Ellis-Van creveld syndrome.
Dental dysplasia in incontinentia pigmenti achromians (Ito): an unusual form.
A case of incontinentia pigmenti achromians with acute lymphatic leukemia.