idiopathic pulmonary hemosiderosis

Also found in: Acronyms.

id·i·o·path·ic pul·mo·nar·y he·mo·sid·er·o·sis

a rare, generally fatal disease of unknown cause, typically affecting small children; characterized by infiltration of pulmonary alveoli with hemosiderin-containing macrophages progressing to diffuse pulmonary fibrosis. Clinical features include recurrent pulmonary hemorrhages, anemia, dyspnea, and cardiorespiratory failure.

idiopathic pulmonary hemosiderosis

Clinical immunology A rare possibly autoimmune condition affecting children < age 10 characterized by hemosiderin deposition in lungs Clinical Recurrent hemoptysis, anemia, weakness, clubbing, hepatosplenomegaly Prognosis Poor, recurrent episodes; death often in 5 yrs due to cor pulmonale; it may be associated with celiac disease and improve with a gluten-free diet. See Hemosiderosis.


Wilhelm, 1884-1964.
Ceelen-Gellerstedt syndrome - repeated sudden attacks of dyspnea and hemoptysis leading to diffuse pulmonary hemosiderosis. Synonym(s): idiopathic pulmonary hemosiderosis
References in periodicals archive ?
Idiopathic pulmonary hemosiderosis presenting in an adult: A case report and review of the literature.
Prognosis in adult patients with idiopathic pulmonary hemosiderosis.
Long-term clinical follow-up of adult idiopathic pulmonary hemosiderosis and celiac disease.
Despite the unknown precise etiology, the association (Lane-Hamilton syndrome) between the Celiac disease and the idiopathic pulmonary hemosiderosis (IPH) is increasingly recognized now.
Eight Years Follow-up of a Case with Idiopathic Pulmonary Hemosiderosis After Corticosteroid Therapy.
Long-term prednisone and azathioprine treatment of a patient with idiopathic pulmonary hemosiderosis.
Effectiveness of chloroquine therapy in idiopathic pulmonary hemosiderosis.
Release of inflammatory mediators after cow's milk intake in a new born with idiopathic pulmonary hemosiderosis.
Idiopathic pulmonary hemosiderosis is a rare cause of iron deficiency anemia in childhood.

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