congenital ichthyosiform erythroderma

(redirected from ichthyosiform erythroderma)


abnormal redness of the skin over widespread areas of the body.
congenital ichthyosiform erythroderma a generalized hereditary dermatitis with scaling, occurring in a bullous form (epidermolytic hyperkeratosis) and a nonbullous form (lamellar ichthyosis).
erythroderma desquamati´vum Leiner's disease.
psoriatic erythroderma a generalized psoriasis vulgaris, showing the chemical characteristics of exfoliative dermatitis.

con·gen·i·tal ich·thy·o·si·form e·ryth·ro·der·ma

a genodermatosis characterized by diffuse chronic erythema and scale formation which may be separated into bullous and nonbullous forms.

con·gen·i·tal ich·thy·o·si·form e·ryth·ro·der·ma

(kŏn-jen'i-tăl ik'thē-ō'si-fōrm ĕ-rith'rō-dĕr'mă)
A genodermatosis characterized by diffuse chronic erythema and scale formation, which occurs in bullous and nonbullous forms.
Synonym(s): ichthyosiform erythroderma.


Antonino, Italian physician, 1872-1950.
Carini syndrome - skin disease of the newborn characterized by fissures and shedding of membrane encasing the body to reveal red skin underneath. Synonym(s): alligator baby; congenital ichthyosiform erythroderma; lamellar desquamation of the newborn; lamellar ichthyosis


Earl Weldon, U.S. dermatologist, 1893–.
Comèl-Netherton syndrome - Synonym(s): Netherton syndrome
Netherton syndrome - brittle hair; atopic manifestations. Synonym(s): Comèl-Netherton syndrome; congenital ichthyosiform erythroderma
References in periodicals archive ?
The 3 major types of autosomal recessive congenital ichthyosis are Harlequin ichthyosis, lamellar ichthyosis, and congenital ichthyosiform erythroderma.
In 1902, Brocq5described ichthyosis hystrix as an atypical form of congenital bullous ichthyosiform erythroderma.
It may result from a pre-existing dermatoses or underlying lymphoma, drug eruptions, hereditary causes eg: ichthyosiform erythroderma.
The condition has to be differentiated from non-bullous ichthyosiform erythroderma, X-linked ichthyosis, Chanarin-Dorfman syndrome and Trichothiodystrophy.
Observation of lipid vacuoles in neutrophils (Jordan's anomaly) in peripheral blood smears in patients with ichthyosiform erythroderma is diagnostic.
CHILD Sendromu (Congenital Hemidysplasia Ichthyosiform Erythroderma Limb Defects)
She was diagnosed as having congenital ichthyosiform erythroderma, a condition that affects just one in 300,000 children.
Hypnosis has been found useful to treat a number of skin disorders including acne excoriee, alopecia areata, atopic dermatitis, congenital ichthyosiform erythroderma, dyshidrotic dermatitis, erythromelalgia, furuncles, glossodynia, herpes simplex, hyperhidrosis, ichthyosis vulgaris, lichen planus, neurodermatitis, nummular dermatitis, postherpetic neuralgia, pruritus, psoriasis, rosacea, trichotillomania, urticaria, verruca vulgaris, and vitiligo.
Ichthyosiform erythroderma, hair shaft abnormalities, and mental and growth retardation.
Friedman S, Lindane neurotoxic reaction in nonbullous congenital ichthyosiform erythroderma.
Friedman[7] reported a case of a boy aged 3 years 9 months who had congenital ichthyosiform erythroderma but no history of seizures.
NASDAQ:CLGY; Warrants:CLGYW), with headquarters in Foster City, Thursday said it had received from the Food and Drug Administration (FDA) a $400,000 Orphan Drug grant for its Phase III study to evaluate the safety and efficacy of the topical drug Glylorin for the treatment of congenital ichthyosiform erythroderma, a disfiguring skin disease.